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This Concept Map, created with IHMC CmapTools, has information related to: case 1-1, GSD type 1b: G6Pase transporter deficiency leads to no glycogenolysis no gluconeogenesis, vomiting which by aspiration can cause lung infection = fluid in lungs, lung infection = fluid in lungs causes noisy breathing, blow off CO2 and decrease pH causes low pCO2 in blood, O2 exchange causes low pO2 in blood, lung infection = fluid in lungs causes fever, congestion, need for antibiotics, no glycogenolysis no gluconeogenesis results in build up of pyruvate, decreased blood pH causes tachnypea, over-abundance of glycogen stored in liver causes hepatomegaly, increase in epinephrine causes clammy, sweaty skin, tachnypea in order to blow off CO2 and decrease pH, decreased hematocrit can cause spleenomegaly, extreme hypoglycemia and no glucose in the urine caused need for glucose I.V. after birth, build up of pyruvate causes high plasma lactate levels, increased plasma KB concentrations causes KBs in the urine, increases in glycogen in spleen causes spleenomegaly, no glycogenolysis no gluconeogenesis causes extreme hypoglycemia and no glucose in the urine, no glycogenolysis no gluconeogenesis leads to increased plasma KB concentrations, increased plasma KB concentrations leads to decreased blood pH, no glycogenolysis no gluconeogenesis leads to increases in glycogen in spleen